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Thank you for the kind words and feedback!! As far as hearing loss in OI is concerned, this is a great question as their is some discrepancy on the form of hearing loss as detected during testing. You would not be incorrect in suggesting conductive hearing loss as a possibility in this patient population. According to this article published in 2011 on NCBI, "It is frequently reported that conductive hearing loss is found in younger patients with OI, whereas sensorineural hearing loss is found more in older patients with OI [17, 19, 21, 23, 28]. This view is not uniform as one study has reported that hearing loss in OI is most frequently sensorineural in origin [29] in the initial presentation. The etiology of sensorineural hearing loss in OI has not been definitively determined but may be a consequence of atrophy of the cochlear hair cells and the stria vascularis as well as from abnormal bone formation in the cochlea and surrounding structures." Article: www.ncbi.nlm.nih.gov/pmc/articles/PMC3335494/